What is Pseudopapillary neoplasm?

Solid pseudopapillary tumor (SPT) of the pancreas is a rare neoplasm, usually characterized by a well encapsulated mass, with low malignant potential. It occurs predominantly in young females, in their third decade of life.

What causes Pseudopapillary tumor?

Solid-pseudopapillary neoplasm (SPN) of the pancreas also known as Frantz’s tumor is an uncommon tumor that mainly occurs in females in their second to fourth decades of life [1]. It accounts for less than one percent of pancreatic tumors and typically arises from the pancreatic tail [2].

Is a Frantz tumor cancer?

It has a low grade malignant potential manifested by invasion of the capsule and contiguous structures. The cell of origin of these rare tumours is unknown; investigators have suggested an origin from primordial pancreatic cells and it has been classified under neoplasms of indeterminate type [4].

What is a cystic pancreatic neoplasm?

Pancreatic cystic neoplasms are fluid-filled sacs (cysts) within the pancreas. Pancreatic cysts are usually found when patients undergo abdominal imaging for other reasons. A Patient Page on types of pancreatic cysts was published in the September 20, 2016, issue of JAMA.

What is Pseudopapillary tumor of the pancreas?

Solid pseudopapillary tumor, otherwise known as solid and cystic tumor or Frantz tumor, is an unusual form of pancreatic carcinoma. Its natural history differs from the more common pancreatic adenocarcinoma in that it has a female predilection, is more indolent, and carries a better prognosis.

Is Solid Pseudopapillary tumor cancer?

Solid pseudopapillary tumor of the pancreas is a rare malignancy. Survival following primary resection approaches 95% at 5 years. Metastatic disease, although rare, usually involves the liver and/or peritoneum.

What is serous cystadenoma pancreas?

Pancreatic serous cystadenomas are benign neoplasms composed of numerous small cysts that are arrayed in a honeycomb-like formation. There can be significant variation in locule size (1-20 mm) 2-4. Most individual cysts are typically <10 mm 12.

What are neoplasms?

(NEE-oh-PLA-zum) An abnormal mass of tissue that forms when cells grow and divide more than they should or do not die when they should. Neoplasms may be benign (not cancer) or malignant (cancer). Benign neoplasms may grow large but do not spread into, or invade, nearby tissues or other parts of the body.

Should I worry about a cyst on my pancreas?

When to see a doctor Rarely, cysts can become infected. See a doctor if you have a fever and persistent abdominal pain. A ruptured pancreatic cyst can be a medical emergency, but fortunately is rare. A ruptured cyst can also cause infection of the abdominal cavity (peritonitis).

When do you need surgery for a pseudopapillary neoplasm?

It can occur in both men and women older than 50. Depending on its location and other factors, IPMN may require surgical removal. Solid pseudopapillary neoplasms are usually situated in the body or tail of the pancreas and occur most often in women younger than 35. They are rare and sometimes cancerous.

How is solid pseudopapillary neoplasm of pancreas treated?

How is Solid-Pseudopapillary Neoplasm of Pancreas Treated? 1 The treatment for choice for Pancreatic Solid-Pseudopapillary Neoplasm is a complete removal… 2 For tumors that are noted to be malignant, a combination therapy that includes radiation therapy… 3 Post-operative care is important: A minimal physical activity is advised,…

What is the prognosis for Solid pseudopapillary tumor?

The prognosis is favorable even in the presence of distant metastasis. Although surgical resection is generally curative, a close follow-up is advised in order to diagnose a local recurrence or distant metastasis and choose the proper therapeutic option for the patient.

Which is the best chemotherapy for pseudopapillary carcinoma?

We analyze a case of a 36-year-old female patient treated with chemotherapy due to advanced stage of solid pseudopapillary tumors. Among a number of administered chemotherapeutic regimens – Folfox-4 (folinic acid+fluorouracil+oxaliplatin) gave particularly good results and was well tolerated, with few adverse effects.